肖英明,廖 洪,谭 政.肾上皮样血管平滑肌脂肪瘤临床特点及预后分析[J].肿瘤学杂志,2016,22(7):579-582.
肾上皮样血管平滑肌脂肪瘤临床特点及预后分析
An Analysis on the Clinical Features and Prognosis of Renal Epithelioid Angiomyolipoma
投稿时间:2015-10-27  
DOI:10.11735/j.issn.1671-170X.2016.07.B011
中文关键词:  肾脏肿瘤  上皮样血管平滑肌脂肪瘤  预后
英文关键词:renal neoplasms  epithelioid,angiomyolipoma  prognosis
基金项目:
作者单位
肖英明 四川省肿瘤医院 
廖 洪 四川省肿瘤医院 
谭 政 四川省肿瘤医院 
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中文摘要:
      摘 要:[目的] 探讨肾上皮样血管平滑肌脂肪瘤(EAML)的临床特点、诊治及预后。 [方法] 回顾性分析8例肾EAML患者的临床特点、诊治及预后的临床资料。 [结果] 8例患者均行了手术治疗,术后病理及免疫组化符合肾EAML诊断。随访时间为5~98个月,平均47个月,无瘤生存6例,另2例生存时间分别为9个月和21个月。[结论] EAML是具有恶性潜能的血管平滑肌脂肪瘤特殊亚型。治疗方案首选手术切除,术后需严密随访,由于其对放化疗及靶向治疗不敏感,一旦肿瘤复发转移,预后差。
英文摘要:
      Abstract:[Purpose] To investigate the clinical features,diagnosis,treatment and prognosis of the renal epithelioid angiomyolipoma(EAML). [Methods] The clinical features,diagnosis,treatment and prognosis of the 8 cases with renal EAML were analyzed retrospectively. [Results] All the 8 cases were treated by surgery. Renal EAML was proved by pathological and immunohistochemical analysis. All patients were followed up for 47months(ranging from 5 to 98 months).Six cases survived with tumor-free,and the survival of other 2 cases was 9 months and 21 months. [Conclusion] EAML is a special subtype of AML with malignant potential. The preferred treatment regimen is surgery,and follow-up is needed after surgery. Because of EAML is not sensitive to chemotherapy,radiotherapy and targeted therapy,the prognosis is poor in patients with tumor recurrence and metastasis.
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